- ISSN: 0253-8253
- EISSN: 2227-0426
-
oa Unusual thoracic tumor in a teenager: A rare occurrence
- Source: Qatar Medical Journal, Volume 2022, Issue 1, Jun 2022, 12
-
- 20 August 2021
- 18 November 2021
- 01 March 2022
Abstract
Pleuropulmonary blastoma (PPB) is a rare malignant lung tumor in the pediatric population and occurs mainly in young children. Its clinical presentation is usually nonspecific. We report a rare occurrence of this tumor in a 15-year-old girl, who presented with symptoms mimicking respiratory tract infection and was nonresponsive to the initial treatment. Imaging investigations revealed a large solid lesion in the left hemithorax with a mass effect on the adjacent structures. Biopsy demonstrated primitive cells with blastematous appearances, and the stroma cells were positive for vimentin and desmin, consistent with PPB. Unfortunately, she died from neutropenic sepsis while undergoing chemotherapy. This report highlights the epidemiology of PPB, its imaging and histopathological features, overview of prognosis, and clinical management.
