1887
Volume 2014, Issue 2
  • ISSN: 2305-7823
  • EISSN:

Abstract

The atrioventricular (AV) valves are complex anatomical structures which perform sophisticated functions.1 A wide spectrum of malformations of these valves can occur in patients with AV septal defects. We here describe the anatomic and functional abnormalities of a rare form of the disease, where two valves connected the right atrium to both the right and left ventricles, in addition to a third valve that connected the left atrium to the left ventricle, with no evidence of regurgitation or cyanosis in spite of the relatively large communication between the right atrium and the left ventricle. In addition, the patient had severe subaortic stenosis. The pathophysiology, hemodynamics and method of repair of the condition are discussed.

Loading

Article metrics loading...

/content/journals/10.5339/gcsp.2014.32
2014-09-01
2024-03-28
Loading full text...

Full text loading...

/deliver/fulltext/gcsp/2014/2/gcsp.2014.32.html?itemId=/content/journals/10.5339/gcsp.2014.32&mimeType=html&fmt=ahah

References

  1. Yacoub MH, Cohn LH. Novel approaches to cardiac valve repair: from structure to function: Part I. Circulation 2004 Mar 2; 109:8:942950.
    [Google Scholar]
  2. Kaski JP, Wolfenden J, Josen M, Daubeney PEF, Shinebourne E a. Can atrioventricular septal defects exist with intact septal structures? Heart 2006 Jun; 92:6:832835.
    [Google Scholar]
  3. Anderson RH, Spicer D. Anatomy of Common Atrioventricular Junction With Complex Associated Lesions. World J Pediatr Congenit Hear Surg. 2010 Apr 1; 1:1:112118.
    [Google Scholar]
  4. Warnes C, Somerville J. Double mitral valve orifice in atrioventricular defects. Br Heart J. 1983 Jan; 49:1:5964.
    [Google Scholar]
  5. Hosny H, AbdelSalam S, Mohsen T, Afifi A. Double orifice left AV valve with partial atrio-ventricular septal defect. Aswan Hear Cent Sci Pract Ser. 2011 Dec; 2011:2:18.
    [Google Scholar]
  6. Praagh R Van. What are double-outlet left atrium and double-outlet right atrium? Ann Pediatr Cardiol. 2013 Jul; 6:2:155157.
    [Google Scholar]
  7. Gnanapragasam J, Houston A, Anderson RH. Double outlet left atrium with double inlet left ventricle and discordant atrioventricular connection. Cardiol Young. 1991;1:155157.
    [Google Scholar]
  8. Edwin F, Kinsley RH, Mamorare HM, Govendrageloo K. The spectrum of double-outlet right atrium including hearts with three atrioventricular valves. Eur J Cardiothorac Surg. 2012 Apr; 41:4:947949.
    [Google Scholar]
  9. Shetkar SS, Kothari SS. Double-outlet left atrium: Ventriculo-atrial malalignment defect. Ann Pediatr Cardiol. 2013 Jul; 6:2:158161.
    [Google Scholar]
  10. Anderson RH. How best to explain unexpected arrangements of the atrioventricular valves? Ann Pediatr Cardiol. 2013 Jul; 6:2:152154.
    [Google Scholar]
  11. Kiraly L, Hubay M, Cook AC, Ho SY, Anderson RH. Morphologic features of the uniatrial but biventricular atrioventricular connection. J Thorac Cardiovasc Surg. 2007 Jan; 133:1:229234.
    [Google Scholar]
http://instance.metastore.ingenta.com/content/journals/10.5339/gcsp.2014.32
Loading
/content/journals/10.5339/gcsp.2014.32
Loading

Data & Media loading...

  • Article Type: Research Article
This is a required field
Please enter a valid email address
Approval was a Success
Invalid data
An Error Occurred
Approval was partially successful, following selected items could not be processed due to error